Neurological Involvement in Erdheim-Chester Disease
نویسندگان
چکیده
منابع مشابه
Orbital involvement in Erdheim-Chester disease.
Erdheim-Chester disease is a rare, idiopathic, non-Langerhans' cell, histiocytic disorder. To our knowledge this is only the second case of Erdheim-Chester disease reported in the Chinese population. We describe a 45-year-old woman presenting with unilateral proptosis and periorbital xanthelasma. Histopathological examination revealed a xanthogranulomatous lesion expressing CD68, but negative f...
متن کاملCardiovascular Involvement in Erdheim–Chester Disease
Erdheim-Chester disease (ECD) is a rare, multiorgan, non-Langerhans cell histiocytosis of uncertain origin, characterized by systemic xanthogranulomatous infiltration from CD68+CD1a- histiocytes. Skeletal involvement is present in up to 96% of cases with bilateral osteosclerosis of meta-diaphysis of long bones. Furthermore, in more than 50% of cases there is 1 extraskeletal manifestation. In th...
متن کاملNeurological manifestations in Erdheim-Chester disease: Two case reports.
Erdheim-Chester disease (ECD) is a rare form of non-Langerhans cell histiocytosis characterised by multiorgan xanthogranulomatous infiltration of histiocytes (CD68+/CD1−). Two highly suggestive characteristics of this disease are sclerosis of the long bones and perirenal fat infiltration. The central nervous system (CNS) involvement occurs in 30% to 50% of cases and is the main predictor of a p...
متن کاملErdheim-Chester Disease
Erdheim-Chester disease (ECD) is a rare, xanthogranulomatous, non-Langerhans cell histiocytosis with frequent systemic involvement. Although the diagnosis is based on characteristic histological and radiological findings, its identification can be challenging because of its heterogeneous presentation. Osteosclerosis of long bones, often associated with bone pain, is the most common initial mani...
متن کاملErdheim-chester disease.
Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis of unknown etiology, characterized by multi-organ involvement. ECD is usually diagnosed on the basis of characteristic radiologic and histopathological findings. Lesions may be skeletal and/or extraskeletal in location, and may include the skin, lung, heart, and central nervous system. We describe here a 68-year-old man ...
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ژورنال
عنوان ژورنال: Journal of Clinical Neurology
سال: 2016
ISSN: 1738-6586,2005-5013
DOI: 10.3988/jcn.2016.12.1.115